Glucose-6-phosphate dehydrogenase (G6PDH)
Fa'amatalaga
O le le lava o le Glucose 6 phosphate dehydrogenase (G6PD) ose tulaga tuufaasolo lea e malepe ai sela mumu (hemolysis) pe a aafia le tino i ni mea'ai, fualaau faasaina, faama'i po o le atuatuvale.E tupu pe a misi se tagata pe maualalo le maualuga ole enzyme glucose-6-phosphate dehydrogenase.O lenei enzyme e fesoasoani i sela mūmū e galue lelei.O fa'ailoga i le taimi o le fa'ama'i toto e ono aofia ai le mimi pogisa, vaivai, sesega, saosaoa le tātā o le fatu, le manava, ma le samasama o le pa'u (jaundice).O le faaletonu o le G6PD o lo'o tu'ufa'atasia ile X-linked recessive ma fa'ailoga e sili atu ona taatele i tama (aemaise Aferika Amerika ma i latou mai nisi vaega o Aferika, Asia, ma le Metitirani).E mafua mai i suiga o le kenera ile gene G6PD.
Glucose-6-Phophate Dehydrogenase (G-6-PDH) e aofia ai vaega laiti e lua o le mamafa mole mole tutusa.O le faʻasologa o le amino acid o le monomer ua faʻasalalau. G-6-PDH ua faʻaaogaina i suʻega mo nicotinamide adenine dinucleotide ma tissue pyridine nucleotides.G-6-PDH e mafai ona toe fa'agaoioia mai vaifofo fa'ama'i urea.
Glucose 6-phosphate dehydrogenase ose enzyme fa'atulafonoina autu i le laasaga muamua o le auala pentose phosphate.G-6-P-DH faʻamaʻiina le kulukose-6-phosphate i luma o le NADP+ e maua ai le 6-phosphogluconate.Polyacrylamide gel electrophoresis, staining gaoioiga, ma anti-fefe G-6-PDH antibody immunoblotting suʻesuʻega ua faʻaalia ai o le G-6-PDH o se glycoprotein.
Fa'atonuga vaila'au
Mataupu Faavae o Tali
D-Glucose-6-phosphate + NAD+→D-Glucono-δ-lactone-6-phosphate + NADH+H+
Fa'amatalaga
Mea Su'ega | Fa'amatalaga |
Fa'amatalaga | Pa'u pa'epa'e amorphous, lyophilized |
Gaoioiga | ≥150U/mg |
Mama (SDS-PAGE) | ≥90% |
Solubility (10mg pa'u/ml) | manino |
NADH/NADPH oxidase | ≤0.1% |
Glutathione reductase | ≤0.001% |
Phosphoglucose isomerase | ≤0.001% |
Creatine phosphokinase | ≤0.001% |
6-Phosphogluconate dehydrogenase | ≤0.01% |
Myokinase | ≤0.01% |
Hexokinase | ≤0.001% |
Felauaiga ma le teuina
Felauaiga: Ambient
Teuina:Teu i le 2-8°C
Fautuaina le toe su'egaSoifua:2 tausaga